Whole body composition analysis by the BodPod air-displacement plethysmography method in children with Phenylketonuria shows a higher body fat percentage

Monique Albersen; Marjolein Bonthuis; Nicole M. De Roos; Dorine A.M. Van Den Hurk; Ems Carbasius Weber; Margriet M.W.B. Hendriks; Monique G.M. De Sain-Van Der Velden; Tom J. De Koning; Gepke Visser

doi:10.1007/s10545-010-9149-8

Whole body composition analysis by the BodPod air-displacement plethysmography method in children with Phenylketonuria shows a higher body fat percentage

Monique Albersen
, Marjolein Bonthuis
, Nicole M. De Roos
, Dorine A.M. Van Den Hurk
, Ems Carbasius Weber
, Margriet M.W.B. Hendriks
, Monique G.M. De Sain-Van Der Velden
, Tom J. De Koning
, Gepke Visser^*

^*Corresponding author for this work

Research output: Contribution to journal › Article › Academic › peer-review

Abstract

Background Phenylketonuria (PKU) causes irreversible central nervous system damage unless a phenylalanine (PHE) restricted diet with amino acid supplementation is maintained. To prevent growth retardation, a protein/amino acid intake beyond the recommended dietary protein allowance is mandatory. However, data regarding disease and/or diet related changes in body composition are inconclusive and retarded growth and/or adiposity is still reported. The BodPod whole body air-displacement plethysmography method is a fast, safe and accurate technique to measure body composition. Aim To gain more insight into the body composition of children with PKU. Methods Patients diagnosed with PKU born between 1991 and 2001 were included. Patients were identified by neonatal screening and treated in our centre. Body composition was measured using the BodPod system (Life Measurement Incorporation

Original language	English
Pages (from-to)	S283-S288
Number of pages	6
Journal	Journal of inherited metabolic disease
Volume	33
Issue number	SUPPL. 3
DOIs	https://doi.org/10.1007/s10545-010-9149-8
Publication status	Published - Dec 2010
Externally published	Yes

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Albersen, M., Bonthuis, M., De Roos, N. M., Van Den Hurk, D. A. M., Carbasius Weber, E., Hendriks, M. M. W. B., De Sain-Van Der Velden, M. G. M., De Koning, T. J., & Visser, G. (2010). Whole body composition analysis by the BodPod air-displacement plethysmography method in children with Phenylketonuria shows a higher body fat percentage. Journal of inherited metabolic disease, 33(SUPPL. 3), S283-S288. https://doi.org/10.1007/s10545-010-9149-8

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title = "Whole body composition analysis by the BodPod air-displacement plethysmography method in children with Phenylketonuria shows a higher body fat percentage",

abstract = "Background Phenylketonuria (PKU) causes irreversible central nervous system damage unless a phenylalanine (PHE) restricted diet with amino acid supplementation is maintained. To prevent growth retardation, a protein/amino acid intake beyond the recommended dietary protein allowance is mandatory. However, data regarding disease and/or diet related changes in body composition are inconclusive and retarded growth and/or adiposity is still reported. The BodPod whole body air-displacement plethysmography method is a fast, safe and accurate technique to measure body composition. Aim To gain more insight into the body composition of children with PKU. Methods Patients diagnosed with PKU born between 1991 and 2001 were included. Patients were identified by neonatal screening and treated in our centre. Body composition was measured using the BodPod system (Life Measurement Incorporation",

author = "Monique Albersen and Marjolein Bonthuis and \{De Roos\}, \{Nicole M.\} and \{Van Den Hurk\}, \{Dorine A.M.\} and \{Carbasius Weber\}, Ems and Hendriks, \{Margriet M.W.B.\} and \{De Sain-Van Der Velden\}, \{Monique G.M.\} and \{De Koning\}, \{Tom J.\} and Gepke Visser",

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year = "2010",

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doi = "10.1007/s10545-010-9149-8",

language = "English",

volume = "33",

pages = "S283--S288",

journal = "Journal of inherited metabolic disease",

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Albersen, M, Bonthuis, M, De Roos, NM, Van Den Hurk, DAM, Carbasius Weber, E, Hendriks, MMWB, De Sain-Van Der Velden, MGM, De Koning, TJ & Visser, G 2010, 'Whole body composition analysis by the BodPod air-displacement plethysmography method in children with Phenylketonuria shows a higher body fat percentage', Journal of inherited metabolic disease, vol. 33, no. SUPPL. 3, pp. S283-S288. https://doi.org/10.1007/s10545-010-9149-8

Whole body composition analysis by the BodPod air-displacement plethysmography method in children with Phenylketonuria shows a higher body fat percentage. / Albersen, Monique; Bonthuis, Marjolein; De Roos, Nicole M. et al.
In: Journal of inherited metabolic disease, Vol. 33, No. SUPPL. 3, 12.2010, p. S283-S288.

Research output: Contribution to journal › Article › Academic › peer-review

TY - JOUR

T1 - Whole body composition analysis by the BodPod air-displacement plethysmography method in children with Phenylketonuria shows a higher body fat percentage

AU - Albersen, Monique

AU - Bonthuis, Marjolein

AU - De Roos, Nicole M.

AU - Van Den Hurk, Dorine A.M.

AU - Carbasius Weber, Ems

AU - Hendriks, Margriet M.W.B.

AU - De Sain-Van Der Velden, Monique G.M.

AU - De Koning, Tom J.

AU - Visser, Gepke

N1 - pre-amc

PY - 2010/12

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N2 - Background Phenylketonuria (PKU) causes irreversible central nervous system damage unless a phenylalanine (PHE) restricted diet with amino acid supplementation is maintained. To prevent growth retardation, a protein/amino acid intake beyond the recommended dietary protein allowance is mandatory. However, data regarding disease and/or diet related changes in body composition are inconclusive and retarded growth and/or adiposity is still reported. The BodPod whole body air-displacement plethysmography method is a fast, safe and accurate technique to measure body composition. Aim To gain more insight into the body composition of children with PKU. Methods Patients diagnosed with PKU born between 1991 and 2001 were included. Patients were identified by neonatal screening and treated in our centre. Body composition was measured using the BodPod system (Life Measurement Incorporation

AB - Background Phenylketonuria (PKU) causes irreversible central nervous system damage unless a phenylalanine (PHE) restricted diet with amino acid supplementation is maintained. To prevent growth retardation, a protein/amino acid intake beyond the recommended dietary protein allowance is mandatory. However, data regarding disease and/or diet related changes in body composition are inconclusive and retarded growth and/or adiposity is still reported. The BodPod whole body air-displacement plethysmography method is a fast, safe and accurate technique to measure body composition. Aim To gain more insight into the body composition of children with PKU. Methods Patients diagnosed with PKU born between 1991 and 2001 were included. Patients were identified by neonatal screening and treated in our centre. Body composition was measured using the BodPod system (Life Measurement Incorporation

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SP - S283-S288

JO - Journal of inherited metabolic disease

JF - Journal of inherited metabolic disease

IS - SUPPL. 3

ER -

Whole body composition analysis by the BodPod air-displacement plethysmography method in children with Phenylketonuria shows a higher body fat percentage

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